From the Department of Orthopedic Surgery, Tehran University of Medical Sciences, Tehran, Iran (Dr. Zargarbashi), Department of Orthopedic Surgery, Sina Hospital, Tehran University of Medical Sciences, Tehran, Iran (Dr. Baghban), Joint Reconstruction Research Center, Tehran University of Medical sciences, Tehran, Iran (Dr. Moharrami), Department of Orthopedic Surgery, Sina Hospital, Tehran University of Medical Sciences, Tehran, Iran (Dr. Basti).
J Am Acad Orthop Surg Glob Res Rev. 2023 Jun 12;7(6). doi: 10.5435/JAAOSGlobal-D-22-00046. eCollection 2023 Jun 1.
It is a rare condition defined by congenital pseudarthrosis of the fibula (CPF), which may be associated with neurofibromatosis (NF) and congenital pseudarthrosis of the tibia. A condition such as this may be symptomatic or asymptomatic, but it requires treatment because of the progression of signs such as ankle valgus and pseudarthrosis of the tibia. There are a number of surgical techniques that can be used to treat this condition, such as tibiofibular fusion, internal fixation, the Ilizarov method, and periosteal flap.
The goal of this study was to describe the treatment results of two patients with CPF using vascularized fibular periosteal flaps.
We described the case of a 5-year-old patient and a 19-month-old patient with isolated CPF. Both patients underwent a distal-based vascularized fibular periosteal flap, and intramedullary fixation was used to treat the patients.
The patients had full union in the pseudarthrosis site, but in the end, both had asymptomatic refracture in the union site. Our experiences showed that it is necessary to use strong intramedullary fixation and bone graft.
腓骨先天性假关节(CPF)是一种罕见的疾病,可能与神经纤维瘤病(NF)和胫骨先天性假关节有关。这种疾病可能有症状,也可能无症状,但由于踝关节外翻和胫骨假关节等体征的进展,需要进行治疗。有许多手术技术可用于治疗这种疾病,例如胫腓骨融合、内固定、伊利扎罗夫方法和骨膜瓣。
本研究旨在描述使用带血管腓骨骨膜瓣治疗 2 例 CPF 患者的治疗结果。
我们描述了一例 5 岁和一例 19 个月大的孤立性 CPF 患者的情况。两名患者均接受了带血管腓骨骨膜瓣治疗,并采用髓内固定治疗患者。
患者的假关节部位完全愈合,但最终均在愈合部位出现无症状再骨折。我们的经验表明,有必要使用强有力的髓内固定和植骨。