Jimenez J F
J Surg Oncol. 1986 Aug;32(4):238-44. doi: 10.1002/jso.2930320413.
Lipoblastoma is a rare benign neoplasm of fetal-embryonal fat tissue with a 14% tendency to recur. It occurs almost exclusively in infants and children. To my knowledge, less than 100 cases, including children and adults, have been reported in the English literature. Two retroperitoneal and one case of mesenteric lipoblastoma, all presenting as a large palpable abdominal mass, are described. Our patients, aged 12 years, 7 months, and 11 months, were treated by total surgical excision of the tumors. They are alive and well 5, 4, and 3 years postoperative, respectively, with no evidence of recurrence and no indication for any adjunctive therapy. Pathologic evaluation was decisive for the best treatment and prognosis.
脂肪母细胞瘤是一种罕见的胎儿 - 胚胎脂肪组织良性肿瘤,复发倾向为14%。它几乎仅发生于婴幼儿和儿童。据我所知,英文文献中报道的包括儿童和成人在内的病例不到100例。本文描述了两例腹膜后脂肪母细胞瘤和一例肠系膜脂肪母细胞瘤,所有病例均表现为可触及的腹部巨大肿块。我们的患者年龄分别为12岁、7个月和11个月,均接受了肿瘤全切手术治疗。术后5年、4年和3年时,他们均存活且状况良好,无复发迹象,也无任何辅助治疗的指征。病理评估对最佳治疗和预后起着决定性作用。