Alshehri Abdullah
Department of Surgery, College of Medicine, King Saud University, Riyadh 11623, Saudi Arabia.
World J Clin Cases. 2023 Jun 16;11(17):4123-4132. doi: 10.12998/wjcc.v11.i17.4123.
Hereditary multiple exostoses is a rare genetic disorder characterized by the growth of multiple osteochondromas affecting primarily long bones. Chest wall lesions may represent a challenge, particularly in pediatric patients. Pain is a common manifestation. However, life-threatening complications can result from direct involvement of adjacent structures. Surgical resection with appropriate reconstruction is often required.
A 5-year-old male who was diagnosed with hereditary multiple exostoses presented with significant pain from a large growing chest wall exostosis lesion. After appropriate preoperative investigations, he underwent surgical resection with reconstruction of his chest wall using a biologic bovine dermal matrix mesh.
Resection of chest wall lesions in children represents a challenge. Preoperative planning to determine the appropriate reconstruction strategy is essential.
遗传性多发性骨软骨瘤是一种罕见的遗传性疾病,其特征是多发性骨软骨瘤主要累及长骨生长。胸壁病变可能是一项挑战,尤其是在儿科患者中。疼痛是常见表现。然而,相邻结构的直接受累可能导致危及生命的并发症。通常需要进行手术切除并进行适当重建。
一名5岁男性被诊断为遗传性多发性骨软骨瘤,因一个不断生长的大型胸壁骨软骨瘤病变而出现严重疼痛。经过适当的术前检查后,他接受了手术切除,并使用生物牛真皮基质网对胸壁进行了重建。
儿童胸壁病变的切除是一项挑战。术前规划以确定合适的重建策略至关重要。