Department of Oncology, Section Radiation Oncology, Aga Khan University, Karachi, Pakistan
Department of Oncology, Section Radiation Oncology, Aga Khan University, Karachi, Pakistan.
BMJ Case Rep. 2023 Jun 30;16(6):e255438. doi: 10.1136/bcr-2023-255438.
A patient in her early 20s presented with blood-stained sputum and shortness of breath. Initially, she was treated for pneumonia. Later, upon exacerbation of symptoms, further investigations were done which exhibited a left atrial mass causing compression of contralateral atrium. She underwent surgical resection of the mass, which was initially mistaken as myxoma. However, histopathological correlation revealed spindle cell sarcoma with focal myogenic differentiation. This case report highlights the role of Radiation Therapy in adjuvant setting with promising impact on improving local control after R2 resection. Cardiac spindle cell sarcoma, being one of the rarest cardiac tumours reported to date, warrants establishment of a Rare Tumour Multidisciplinary Team for management of such malignancies.
一位 20 岁出头的患者出现咯血和呼吸急促。最初，她被诊断为肺炎并接受治疗。后来，由于症状恶化，进一步的检查显示左心房有一个肿块，导致对侧心房受压。她接受了肿块的手术切除，最初被误诊为粘液瘤。然而，组织病理学相关性显示为具有局灶性肌源性分化的梭形细胞肉瘤。本病例报告强调了放射治疗在辅助治疗中的作用，对 R2 切除后改善局部控制具有积极影响。心脏梭形细胞肉瘤是迄今为止报告的最罕见的心脏肿瘤之一，需要建立一个罕见肿瘤多学科团队来管理此类恶性肿瘤。
