Luntz M, Frank I, Yurovitzki I, Berger G, Sadé J
Am J Otol. 1986 Jul;7(4):282-6.
Perilymph fistulas may manifest themselves either by otologic symptoms, as in cases of small fistulas, or primarily through neurologic symptoms, as with large fistulas. A case history is presented of a 3-year-old girl with recurrent bouts of meningitis who was found to have a large perilymph fistula. She had a right undeveloped cochlea and labyrinth, as well as multiple defects of the medial wall of her middle ear. The only way of preventing the recurrent bouts of bacterial meningitis in cases of large perilymph fistulas is surgical repair. Our conclusion is that, considering the problems involved in cases of large congenital perilymph fistulas, a simple closure of the fistula is not sufficient and the method of choice is obliteration of a deeper structure--such as the vestibule itself.
外淋巴瘘可能表现为耳科症状，如小瘘管病例；或主要表现为神经症状，如大瘘管病例。本文介绍了一名3岁女童的病史，该女童反复患脑膜炎，被发现患有一个大的外淋巴瘘。她右侧耳蜗和迷路未发育，中耳内侧壁有多处缺损。对于大外淋巴瘘病例，预防细菌性脑膜炎反复发作的唯一方法是手术修复。我们的结论是，考虑到大型先天性外淋巴瘘病例所涉及的问题，单纯封闭瘘管是不够的，首选方法是消除更深层结构，如前庭本身。
