Department of Neurology, Wroclaw Medical University, Wroclaw, Poland.
Department of General and Interventional Radiology and Neuroradiology, Wroclaw Medical, University, Wroclaw, Poland.
Clin Neurol Neurosurg. 2023 Sep;232:107871. doi: 10.1016/j.clineuro.2023.107871. Epub 2023 Jul 3.
Hypertrophic olivary degeneration (HOD) is a rare condition caused by lesions of the dentato-rubro-olivary pathway, usually bilateral. We presented a case of a 64-year old male with HOD caused by a unilateral, posterior pontine cavernoma. The patient has not developed the typical palate myoclonus until recently. Isolated hand myoclonus with coexisting asterixis was present for years. This case shows unique HOD symptomatology and emphasizes the important role of MRI in the differential diagnosis of monomelic myoclonus.
橄榄体脑桥小脑萎缩（HOD）是一种由齿状核红核橄榄束病变引起的罕见疾病，通常为双侧。我们报告了一例由单侧、后部脑桥海绵状血管瘤引起的 64 岁男性 HOD 病例。该患者直到最近才出现典型的腭阵挛。多年来一直存在孤立的手阵挛伴协同性震顫。本例显示了独特的 HOD 症状，并强调了 MRI 在单发性肌阵挛鉴别诊断中的重要作用。
