Hayasaka S, Shiono T, Mizuno K, Sasayama C, Akiya S, Tanaka Y, Hayakawa M, Miyake Y, Ohba N
Br J Ophthalmol. 1986 Aug;70(8):612-4. doi: 10.1136/bjo.70.8.612.
We examined 15 Japanese patients who had gyrate atrophy of the choroid and retina with hyperornithinaemia. Their visual acuities fell to 0.2 or worse in the second or third decade of life. Myopia developed late in the first decade, and the refractions decreased to -10 or -15 dioptres at age 20. Tunnel vision developed at approximately age 20. Our results suggested that the visual functions of Japanese patients were worse in the third decade or later than similarly affected Finnish patients.
我们检查了15名患有鸟氨酸血症伴脉络膜和视网膜回旋性萎缩的日本患者。他们的视力在生命的第二个或第三个十年降至0.2或更差。近视在第一个十年后期出现，20岁时屈光度降至-10或-15。管状视野大约在20岁时出现。我们的结果表明，日本患者在第三个十年及以后的视觉功能比受类似影响的芬兰患者更差。
