Otieno Daniel Odhiambo, Malik Janan, Wabwire Benjamin
Department of Plastic, Reconstructive and Aesthetic Surgery University of Nairobi School of Medicine, Nairobi, Kenya.
Department of Plastic, Reconstructive and Aesthetic Surgery University of Nairobi School of Medicine, Nairobi, Kenya.
Int J Surg Case Rep. 2023 Aug;109:108512. doi: 10.1016/j.ijscr.2023.108512. Epub 2023 Jul 19.
Low grade Fibromyxoid sarcoma (LGFMS) is a rare soft tissue sarcoma. LGFMS has an indolent clinical behavior but it is prone for late local recurrence and metastasis. In children it is commonly seen in the subcutaneous tissues relative to adults where it presents in deep soft tissues. These patients are best managed in a specialized unit with a multidisciplinary team. For patients with sarcoma, wide local excision remains the treatment of choice. Large complex abdominal wall defects present a unique reconstructive challenge to the surgeon following tumor removal.
Here, we present a case of a 9-year old pediatric male patient with complex abdominal wall defect post excision of a recurrent fibromyxoid sarcoma, reconstructed with a sandwich omental flap, monofilament polypropylene mesh (Bard® Mesh) and split-thickness skin graft (STSG).
Despite the success of covering the defect, the patient still had quite a bit of morbidity with the following:abdominal hernia defect and tumor recurrence. Our case demonstrates the diagnostic and therapeutic challenges in management of sarcomas hence the need for these patients to be managed through a multidisciplinary approach.
The omental flap is quite versatile, and knowing how to raise it does not require sophisticated microsurgical skills. It adds to the reconstructive surgeon's armamentarium, especially in resource-limited settings.
低度纤维黏液样肉瘤(LGFMS)是一种罕见的软组织肉瘤。LGFMS临床行为惰性,但易发生局部晚期复发和转移。在儿童中,它常见于皮下组织,而在成人中则多见于深部软组织。这些患者最好在由多学科团队组成的专业科室进行治疗。对于肉瘤患者,广泛局部切除仍然是首选治疗方法。肿瘤切除后,巨大复杂的腹壁缺损给外科医生带来了独特的重建挑战。
在此,我们报告一例9岁男性儿科患者,在复发性纤维黏液样肉瘤切除术后出现复杂腹壁缺损,采用网膜三明治皮瓣、单丝聚丙烯网片(巴德网片)和中厚皮片移植(STSG)进行重建。
尽管成功覆盖了缺损,但患者仍有相当多的并发症,如下:腹壁疝缺损和肿瘤复发。我们的病例展示了肉瘤治疗中的诊断和治疗挑战,因此需要通过多学科方法对这些患者进行管理。
网膜皮瓣用途广泛,掌握其掀起方法不需要复杂的显微外科技术。它为重建外科医生增添了手段,尤其是在资源有限的情况下。