Singh Belzinder Pal, Abdul Halim Syurahbil, Yahaya Sahran, Mat Zin Nor Azman, Tuan Sharif Sharifah Emilia, Wan Ismail Wan Faisham
Department of Orthopaedics, School of Medical Sciences, Universiti Sains Malaysia, Kubang Kerian, Kelantan, Malaysia.
Hospital Universiti Sains Malaysia, Kubang Kerian, Kelantan, Malaysia.
Case Rep Oncol. 2023 Jul 3;16(1):478-483. doi: 10.1159/000529895. eCollection 2023 Jan-Dec.
Desmoplastic fibroma is a rare primary benign bone tumour that typically affects the long bones, mandible, and pelvis. It has a similar local aggressiveness to soft tissue fibromatosis. It rarely involves the small bones of the hand. We describe an extremely rare case of desmoplastic fibroma of the proximal phalanx of the hand in a patient who presented with an aggressively enlarging but painless mass on the left ring finger. Radiological features suggested malignancy; however, an initial biopsy revealed fibrotic tissue. Trans-metacarpal amputation of the ring and little fingers and soft tissue reconstruction were performed using a local ulnar-based flap of the little finger. The final histopathological evaluation revealed desmoplastic fibroma. Aggressively growing masses in the hand should be treated according to a sarcoma management protocol, and desmoplastic fibroma should be included in the differential diagnosis.
促结缔组织增生性纤维瘤是一种罕见的原发性良性骨肿瘤，通常累及长骨、下颌骨和骨盆。它与软组织纤维瘤病具有相似的局部侵袭性。它很少累及手部小骨。我们描述了一例极其罕见的手部近节指骨促结缔组织增生性纤维瘤病例，该患者左手环指出现一个迅速增大但无痛的肿块。影像学特征提示为恶性；然而，初步活检显示为纤维化组织。采用基于小指尺侧的局部皮瓣对手指环指和小指进行经掌骨截肢及软组织重建。最终的组织病理学评估显示为促结缔组织增生性纤维瘤。手部迅速生长的肿块应按照肉瘤管理方案进行治疗，促结缔组织增生性纤维瘤应列入鉴别诊断范围。
