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揭开股骨远端骨旁脂肪瘤之谜:一例罕见病例报告

Unraveling the Mystery of Parosteal Lipoma of the Distal Femur: A Rare Case Report.

作者信息

Sathiyaseelan Naveen, Meena Mahaveer, Jhanwar Purushottam

机构信息

Department of Orthopaedics, Jhalawar Medical College, Jhalawar, Rajasthan, India.

出版信息

J Orthop Case Rep. 2023 Jul;13(7):82-85. doi: 10.13107/jocr.2023.v13.i07.3762.

DOI:10.13107/jocr.2023.v13.i07.3762
PMID:37521396
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC10379241/
Abstract

INTRODUCTION

Among all the primary bone tumors and all the type of lipomas, parosteal lipomas stand for <0.1% and 0.3%, respectively, which mostly consists of fully developed adipose tissue with or without a bony component. Patients with this tumor usually have bony lesions (59.2%), necessitating a differential diagnosis of malignant tumors.

CASE REPORT

Here, we analyze a case report of a 9-year-old boy, who developed a parosteal lipoma in the distal femur. A massive, well-defined, lobulated, mostly fat-intensity lesion of 10 cm by 6 cm by 8 cm was seen on an magnetic resonance imaging scan of the right distal femur. After the lump was removed, the pathologically reveals a parosteal lipoma without any malignant changes.

CONCLUSION

Finally, it should be noted that parosteal lipomas are less common neoplasias with no known malignant potential. Since these tumors can be removed with mild impact to nearby structures, the lower limb's functionality is kept intact.

摘要

引言

在所有原发性骨肿瘤以及所有类型的脂肪瘤中,骨旁脂肪瘤分别占比不到0.1%和0.3%,其主要由完全成熟的脂肪组织组成,可伴有或不伴有骨成分。患有这种肿瘤的患者通常有骨病变(59.2%),因此需要与恶性肿瘤进行鉴别诊断。

病例报告

在此,我们分析一例9岁男孩在股骨远端发生骨旁脂肪瘤的病例报告。在右股骨远端的磁共振成像扫描中,可见一个巨大的、边界清晰的、分叶状的、大小为10厘米×6厘米×8厘米的、主要呈脂肪密度的病变。肿块切除后,病理显示为无任何恶性变化的骨旁脂肪瘤。

结论

最后,需要注意的是,骨旁脂肪瘤是罕见的肿瘤,尚无已知的恶性潜能。由于这些肿瘤可以在对附近结构影响较小的情况下切除,下肢功能得以保持完整。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2800/10379241/4f8e757c14bc/JOCR-13-82-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2800/10379241/4c34f183f779/JOCR-13-82-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2800/10379241/d1a405b2cd53/JOCR-13-82-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2800/10379241/d83c3b7b0c76/JOCR-13-82-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2800/10379241/4f8e757c14bc/JOCR-13-82-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2800/10379241/4c34f183f779/JOCR-13-82-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2800/10379241/d1a405b2cd53/JOCR-13-82-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2800/10379241/d83c3b7b0c76/JOCR-13-82-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2800/10379241/4f8e757c14bc/JOCR-13-82-g004.jpg

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本文引用的文献

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Large Parosteal Lipoma without Periosteal Changes.无骨膜改变的大型骨旁脂肪瘤。
Plast Reconstr Surg Glob Open. 2015 Feb 6;3(1):e287. doi: 10.1097/GOX.0000000000000254. eCollection 2015 Jan.
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Lump on back: a rare case of parosteal lipoma of scapula.背部肿块:一例罕见的肩胛骨骨膜下脂肪瘤病例。
Case Rep Radiol. 2014;2014:169157. doi: 10.1155/2014/169157. Epub 2014 Sep 22.
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Parosteal lipoma. Report of 15 new cases and a review of the literature.骨旁脂肪瘤。15例新病例报告及文献复习。
Ann Ital Chir. 2013 Mar-Apr;84(2):229-35.
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Parosteal osteoliposarcoma: a new bone tumor (from imaging to immunophenotype).骨旁骨脂肉瘤:一种新的骨肿瘤(从影像学表现到免疫表型)。
Eur J Radiol. 2013 Dec;82(12):2149-53. doi: 10.1016/j.ejrad.2011.11.035. Epub 2011 Dec 15.
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Intraosseous lipoma: a clinical study of 12 patients.骨内脂肪瘤:12例患者的临床研究
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