Department of Medical Oncology, Dana-Farber Cancer Institute, Boston, MA.
Department of Medicine and Carbone Cancer Center, University of Wisconsin School of Medicine and Public Health, Madison, WI.
Haematologica. 2024 Jan 1;109(1):186-199. doi: 10.3324/haematol.2023.283245.
Despite recent advances in the therapy of diffuse large B-cell lymphoma (DLBCL), many patients are still not cured. Therefore, new therapeutic strategies are needed. The anti-apoptotic B-cell lymphoma 2 (BCL2) gene is commonly dysregulated in DLBCL due to various mechanisms such as chromosomal translocation t(14;18)(q32;q21) and copy number alterations; however, targeting BCL-2 with the selective inhibitor, venetoclax, led to response in only a minority of patients. Thus, we sought to identify a rational combination partner of venetoclax to improve its activity against DLBCL cells. Utilizing a functional assay, dynamic BH3 profiling, we found that the DNA hypomethylating agent decitabine increased mitochondrial apoptotic priming and BCL-2 dependence in DLBCL cells. RNA-sequencing analysis revealed that decitabine suppressed the pro-survival PI3K-AKT pathway and altered the mitochondria membrane composition in DLBCL cell lines. Additionally, it induced a DNA damage response and increased BAX and BAK activities. The combination of decitabine and venetoclax synergistically suppressed proliferation of DLBCL cells both in vitro and in vivo in a DLBCL cell line-derived xenograft mouse model. Our study suggests that decitabine plus venetoclax is a promising combination to explore clinically in DLBCL.
尽管弥漫性大 B 细胞淋巴瘤 (DLBCL) 的治疗最近取得了进展,但许多患者仍未治愈。因此,需要新的治疗策略。抗凋亡 B 细胞淋巴瘤 2 (BCL2) 基因在 DLBCL 中由于各种机制(如染色体易位 t(14;18)(q32;q21) 和拷贝数改变)经常失调;然而,用选择性抑制剂 venetoclax 靶向 BCL-2 仅导致少数患者有反应。因此,我们试图确定 venetoclax 的合理组合伙伴,以提高其对 DLBCL 细胞的活性。利用功能测定、动态 BH3 分析,我们发现去甲基化剂地西他滨增加了线粒体凋亡的引发和 DLBCL 细胞中 BCL-2 的依赖性。RNA 测序分析显示,地西他滨抑制了促生存的 PI3K-AKT 通路,并改变了 DLBCL 细胞系中线粒体膜的组成。此外,它还诱导了 DNA 损伤反应并增加了 BAX 和 BAK 的活性。地西他滨和 venetoclax 的联合在体外和体内 DLBCL 细胞系衍生的异种移植小鼠模型中均协同抑制了 DLBCL 细胞的增殖。我们的研究表明,地西他滨加 venetoclax 是一种很有前途的联合治疗方法,值得在 DLBCL 中进行临床探索。