斯陶费尔综合征黄疸变异型作为1型乳头状肾细胞癌的副肿瘤表现
Icteric Variant of Stauffer Syndrome as a Paraneoplastic Manifestation of Type 1 Papillary Renal Cell Carcinoma.
作者信息
Sorda Juan Antonio, Barreyro Fernando Javier, Rojas German, Greco Daniel Alejandro, Paes Andrea, Avagnina Alejandra, Daruich Jorge, Ballerga Esteban González
机构信息
Department of Gastroenterology and Hepatology, University Hospital "José de San Martín", Faculty of Medicine, University of Buenos Aires, Argentina.
Laboratory of Molecular Biotechnology (BIOTECMOL), Biotechnology Institute of Misiones (INBIOMIS), National University of Misiones, National Scientific and Technical Research Council (CONICET), Argentina.
出版信息
ACG Case Rep J. 2023 Aug 2;10(8):e01111. doi: 10.14309/crj.0000000000001111. eCollection 2023 Aug.
Intrahepatic cholestasis as a paraneoplastic manifestation was first described by Dr. Maurice H. Stauffer in 1961. This paraneoplastic manifestation was primarily associated with renal cell carcinoma characterized by abnormal liver enzymes without hepatic metastasis. Stauffer syndrome is classified into 2 types: classical and jaundice variants. Indeed, the jaundice variant is extremely rare and only described in 13 published cases. We report a case of intrahepatic cholestasis associated with a type 1 papillary renal cell carcinoma with complete resolution after surgical treatment.
肝内胆汁淤积作为一种副肿瘤表现最早于1961年由莫里斯·H·斯托弗博士描述。这种副肿瘤表现主要与肾细胞癌相关，其特征为肝酶异常且无肝转移。斯托弗综合征分为2型：经典型和黄疸型。事实上，黄疸型极为罕见，仅在13例已发表病例中有所描述。我们报告1例与1型乳头状肾细胞癌相关的肝内胆汁淤积病例，手术治疗后完全缓解。
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