Dewana Sudheer Kumar, Parmar Kalpesh Mahesh, Sharma Gopal, Bansal Amit, Panwar Pankaj, Mavuduru Ravimohan S
Dept of Urology, PGIMER, Chandigarh, India.
Urol Case Rep. 2019 Feb 11;24:100841. doi: 10.1016/j.eucr.2019.100841. eCollection 2019 May.
Nonmetastatic hepatic dysfunction known as Stauffer's syndrome is a rare entity. It is commonly associated with clear cell carcinoma of kidney. Rarely it has been reported in cases of prostatic carcinoma, bronchogenic tumor and lymphoproliferative diseases. Stauffer s syndrome presents as elevated alkaline phosphatase, aminotransferases, and prolonged prothrombin time without jaundice. However a very rare variant of Stauffer's syndrome presenting with jaundice has been reported in few case reports of clear cell carcinoma of kidney. But such a presentation in cases of renal sarcomas has not been reported so far. Here we report a unique case of primary synovial sarcoma of kidney presenting as nonmetastatic cholestatic jaundice.
被称为施陶费尔综合征的非转移性肝功能障碍是一种罕见病症。它通常与肾透明细胞癌相关。在前列腺癌、支气管源性肿瘤和淋巴增殖性疾病的病例中很少有报道。施陶费尔综合征表现为碱性磷酸酶、转氨酶升高,凝血酶原时间延长且无黄疸。然而,在少数肾透明细胞癌病例报告中曾报道过一种非常罕见的伴有黄疸的施陶费尔综合征变体。但迄今为止,肾肉瘤病例中尚未有这种表现的报道。在此,我们报告一例表现为非转移性胆汁淤积性黄疸的原发性肾滑膜肉瘤的独特病例。