Rhoda M D, Arous N, Garel M C, Mazarin M, Monplaisir N, Braconnier F, Rosa J, Cohen-Solal M, Galacteros F
Hemoglobin. 1986;10(1):21-31. doi: 10.3109/03630268609072468.
Hb Siriraj is a beta chain variant in which beta 7 (A4) Glu is replaced by a lysine. It has been encountered in association with Hb S in a black man from Martinique. Some properties of Hb Siriraj are compared, particularly, with Hb C [alpha 2 beta 26(A3)Glu----Lys], and a study of its in vitro interaction with Hb S is discussed.
西里拉吉血红蛋白是一种β链变异体,其中β7(A4)谷氨酸被赖氨酸取代。在一名来自马提尼克岛的黑人中,它与镰状细胞血红蛋白同时出现。本文比较了西里拉吉血红蛋白的一些特性,特别是与血红蛋白C [α2β2 6(A3)谷氨酸→赖氨酸]进行了比较,并讨论了其与镰状细胞血红蛋白体外相互作用的研究。