Department of Molecular Medicine, University of Pavia, Pavia, Italy; Molecular Cardiology, IRCCS Istituti Clinici Scientifici Maugeri, Pavia, Italy.
Department of Molecular Medicine, University of Pavia, Pavia, Italy.
Card Electrophysiol Clin. 2023 Sep;15(3):349-365. doi: 10.1016/j.ccep.2023.04.004. Epub 2023 Jun 9.
Arrhythmogenic cardiomyopathy is an umbrella term for a group of inherited diseases of the cardiac muscle characterized by progressive fibro-fatty replacement of the myocardium. As suggested by the name, the disease confers electrical instability to the heart and increases the risk of the development of life-threatening arrhythmias, representing one of the leading causes of sudden cardiac death (SCD), especially in young athletes. In this review, the authors review the current knowledge of the disease, highlighting the state-of-the-art approaches to the prevention of the occurrence of SCD.
致心律失常性右室心肌病是一组心肌遗传性疾病的统称，其特征为心肌进行性纤维脂肪替代。顾名思义，该疾病使心脏电不稳定，增加发生危及生命的心律失常的风险，是导致心源性猝死（SCD）的主要原因之一，尤其是在年轻运动员中。在这篇综述中，作者回顾了该疾病的现有知识，强调了预防 SCD 发生的最新方法。
