Matsuura Rikako, Shimizu Yusuke, Matsuura Naoki, Ntege Edward Hosea, Wada Naoki
Department of Plastic and Reconstructive Surgery, Graduate School of Medicine, University of the Ryukyus, Okinawa 903-0215, Japan.
Department of Pathology and Oncology, Graduate School of Medicine, University of the Ryukyus, Okinawa 903-0215, Japan.
J Clin Med. 2023 Jul 28;12(15):4957. doi: 10.3390/jcm12154957.
Poland syndrome (PS), an uncommon congenital unilateral aplasia of chest wall muscles, may exhibit rare accompanying signs, such as axillary webbing or contractures. The existing literature on the specific management of axillary contractures is limited. In this report, we present the case of a 10-year-old girl with PS manifesting an axillary web containing a fibrous band, which was successfully surgically corrected by a double-opposing Z-plasty. Our surgical approach entailed a meticulous distinction between the deep fibrous band and the superficial cutaneous layer, guided by histopathological findings that indicated the presence of tendon-like tissue, ultimately yielding excellent outcomes. This report will help expand knowledge by highlighting the unique manifestation of PS and emphasizing the importance of employing appropriate treatment approaches. Moreover, addressing both tendon and skin components is essential for optimal contracture release in PS.
波兰综合征(PS)是一种罕见的先天性单侧胸壁肌肉发育不全,可能伴有罕见的体征,如腋窝蹼状畸形或挛缩。关于腋窝挛缩具体治疗方法的现有文献有限。在本报告中,我们介绍了一名10岁患有PS的女孩的病例,其腋窝蹼内含有一条纤维带,通过双反向Z成形术成功进行了手术矫正。我们的手术方法需要在组织病理学结果显示存在腱样组织的指导下,仔细区分深部纤维带和浅表皮肤层,最终取得了良好的效果。本报告将通过突出PS的独特表现并强调采用适当治疗方法的重要性,有助于扩大相关知识。此外,处理腱和皮肤成分对于PS中最佳挛缩松解至关重要。