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经鼻内镜入路治疗小儿脑脊膜膨出。

An Endoscopic Endonasal Attempt at Pediatric Meningoencephalocele Repair.

机构信息

Oakland University William Beaumont School of Medicine, Detroit, MI, USA.

Cedars Sinai Sinus Center of Excellence, Los Angeles, CA, USA.

出版信息

Ear Nose Throat J. 2023 Sep;102(9_suppl):24S-26S. doi: 10.1177/01455613231187760. Epub 2023 Aug 13.

DOI:10.1177/01455613231187760
PMID:37574852
Abstract

Meningoencephalocele is an abnormal skull base protrusion of fluid, brain tissue, and meninges that can lead to nasal obstruction, meningitis, and Cerebrospinal Fluid (CSF) rhinorrhea. This condition can be managed operatively through an open craniotomy or a less invasive endoscopic approach. Here, we report a case of an 18-month-old female who presented with a meningoencephalocele that was part of the Sakoda complex, a rare neurosurgical phenomenon consisting of meningoencephalocele, agenesis of the corpus callosum, and cleft lip/palate. The patient was initially treated with the endoscopic transsphenoidal approach with subsequent open craniotomy.

摘要

脑脊膜膨出是一种颅骨底部异常的液体、脑组织和脑膜突出物,可导致鼻阻塞、脑膜炎和脑脊液(CSF)鼻漏。这种情况可以通过开颅手术或创伤较小的内镜方法进行手术治疗。在此,我们报告了一例 18 个月大的女性患者,她患有脑脊膜膨出,是 Sakoda 综合征的一部分,这是一种罕见的神经外科现象,包括脑脊膜膨出、胼胝体发育不全和唇裂/腭裂。患者最初采用内镜经蝶窦入路治疗,随后进行开颅手术。

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