Kumar Sudesh, Sharma Shivbrat, Chauhan Narvir
Department of Otolaryngology, Head, and Neck Surgery, Dr. Rajendra Prashad Medical College, Himachal Pradesh, India.
Radiodiagnosis, Dr. Rajendra Prashad Medical College, Himachal Pradesh, India.
Oman Med J. 2023 Jul 31;38(4):e537. doi: 10.5001/omj.2023.37. eCollection 2023 Jul.
Congenital cholesteatoma is a rare lesion resulting from failed involution of epidermoid rest cells, which take part in the formation of the mucosa of the middle ear cleft during embryonic development. We report the first case report of a large congenital hypotympanic cholesteatoma with extension to the jugular foramen and carotid canal, in a 13-year-old girl, which was excised successfully by endoscopic-assisted hypotympanotomy infra-cochlear approach.
先天性胆脂瘤是一种罕见的病变,由表皮样残余细胞退化失败所致,这些细胞在胚胎发育过程中参与中耳裂黏膜的形成。我们报告了首例13岁女孩的大型先天性下鼓室胆脂瘤,其病变延伸至颈静脉孔和颈动脉管,通过内镜辅助下鼓室切开术经耳蜗下入路成功切除。