Al-Dairy Alwaleed, Ahmad Reem, Hasan Rawan
Cardiac Surgery, Faculty of Medicine Damascus University Damascus Syria.
Faculty of Medicine Damascus University Damascus Syria.
Clin Case Rep. 2023 Aug 24;11(9):e7826. doi: 10.1002/ccr3.7826. eCollection 2023 Sep.
Awareness of persistent left superior vena cava (PLSVC) with unroofed coronary sinus is crucial. Pre- and perioperative evaluation of this association is necessary for surgical plan. Creating an intra-atrial tunnel to divert LSVC to right atrium without obstructing the mitral valve or the pulmonary veins is the safe surgical approach.
Unroofed coronary sinus syndrome is a rare congenital heart defect representing less than 1% of all atrial septal defect (ASD) types, and may be associated with persistent left superior vena cava (PLSVC) which may be missed during preoperative diagnosis. Herein, we present a case of a 2-year-old patient who underwent an operation for repair of a coronary sinus-type ASD; however, PLSVC was detected intraoperatively. An antra-atrial tunnel has created to divert the flow of PLSVC into the right atrium along with the repair of the ASD.
认识到永存左上腔静脉（PLSVC）合并无顶冠状静脉窦至关重要。对于该关联进行术前和围手术期评估对于手术计划是必要的。创建一个心房内隧道，将左上腔静脉引流至右心房，同时不阻塞二尖瓣或肺静脉，是安全的手术方法。
无顶冠状静脉窦综合征是一种罕见的先天性心脏缺陷，占所有房间隔缺损（ASD）类型的不到1%，并且可能与永存左上腔静脉（PLSVC）相关，而永存左上腔静脉在术前诊断时可能被遗漏。在此，我们报告一例2岁患者，该患者接受了冠状静脉窦型房间隔缺损修复手术；然而，术中检测到永存左上腔静脉。在修复房间隔缺损的同时，创建了一个心房内隧道，将永存左上腔静脉的血流引流至右心房。
