Ramírez Luis Eduardo, Amézquita María Alejandra, Morales Eliana Isabel, Sua Luz Fernanda, Fernández-Trujillo Liliana
Department of Internal Medicine, Pulmonology Fellow Program, Universidad Nacional, Bogotá, Colombia.
Clinical Research Center, Fundación Valle del Lili, Cali, Colombia.
Respir Med Case Rep. 2023 Aug 12;45:101910. doi: 10.1016/j.rmcr.2023.101910. eCollection 2023.
Bronchiolitis obliterans (BO) is a progressive fibrotic process that predominantly affects the small airways and is identified as constrictive bronchiolitis by pathologists. It is commonly associated with allogeneic hematopoietic stem cell transplant (HSCT), lung transplant, exposure to inhaled toxins, post-infectious processes, autoimmune diseases, and sometimes, no known cause. In the latter case, it is referred to as cryptogenic bronchiolitis obliterans. A 52-year-old Hispanic man with a medical history of hypertension, diabetes mellitus, and coronary artery disease was referred to the pulmonary department due to experiencing dyspnea on exertion, intermittent dry cough, and progressive limitation of activities of daily living. Spirometry revealed severe obstructive changes, and chest high-resolution computed tomography showed ground-glass opacities with nodular infiltrates in the upper lobes, leading to a presumptive diagnosis of hypersensitivity pneumonitis. The patient underwent a lung surgical biopsy of the right upper and lower lobes, which revealed extensive constrictive bronchiolitis. Due to the patient's worsening general condition, bilateral lung transplantation succeeded without any further complications. Following the transplantation, the patient showed good recovery and functional improvement. Bronchiolitis obliterans, or constrictive bronchiolitis, has a variable natural history. It is associated with a higher risk of mortality in allogenic HSCT. When BO is secondary to inhalation of toxic gases, it is usually nonprogressive and limited to toxin exposure. Autoimmune diseases or cryptogenic bronchiolitis are rare and have a heterogeneous clinical course. To make a proper diagnosis, clinical history, radiologic and histologic findings must be considered.
闭塞性细支气管炎(BO)是一种进行性纤维化过程,主要影响小气道,病理学家将其鉴定为缩窄性细支气管炎。它通常与异基因造血干细胞移植(HSCT)、肺移植、吸入毒素暴露、感染后过程、自身免疫性疾病相关,有时也无已知病因。在后一种情况下,它被称为隐源性闭塞性细支气管炎。一名52岁的西班牙裔男性,有高血压、糖尿病和冠状动脉疾病病史,因劳力性呼吸困难、间歇性干咳和日常生活活动逐渐受限而被转诊至呼吸科。肺功能检查显示严重的阻塞性改变,胸部高分辨率计算机断层扫描显示上叶有磨玻璃影伴结节状浸润,初步诊断为过敏性肺炎。患者接受了右上叶和下叶的肺手术活检,结果显示广泛的缩窄性细支气管炎。由于患者的一般状况恶化,双侧肺移植成功,无任何进一步并发症。移植后,患者恢复良好,功能改善。闭塞性细支气管炎或缩窄性细支气管炎有不同的自然病程。在异基因HSCT中,它与较高的死亡风险相关。当BO继发于吸入有毒气体时,通常是非进行性的,且局限于毒素暴露。自身免疫性疾病或隐源性细支气管炎很少见,临床病程各异。要做出正确诊断,必须考虑临床病史、影像学和组织学检查结果。