Bradley J D
Ann Rheum Dis. 1986 Sep;45(9):780-2. doi: 10.1136/ard.45.9.780.
Spontaneous pneumomediastinum has not been reported in adult polymyositis or dermatomyositis, either in conjunction with spontaneous pneumothorax or in isolation. Spontaneous pneumothorax has been rarely reported as a complication of rheumatoid arthritis, systemic lupus erythematosus, scleroderma, and childhood dermatomyositis. It is associated with active, progressive pulmonary involvement and a poor prognosis. We describe an adult with dermatomyositis and spontaneous pneumomediastinum with a favourable outcome.
成人多发性肌炎或皮肌炎合并自发性气胸或单独出现自发性纵隔气肿的情况尚未见报道。自发性气胸作为类风湿关节炎、系统性红斑狼疮、硬皮病及儿童皮肌炎的并发症鲜有报道。它与活动性、进行性肺部受累及预后不良相关。我们报道一名患有皮肌炎并伴有自发性纵隔气肿的成人患者,其预后良好。