Duhamel J F, Travert G, Briere S, Wysocki E, Laniece M, Bureau F, Delmas P, Venezia R
Arch Fr Pediatr. 1986 Apr;43(4):229-33.
From a systematic neonatal screening for cystic fibrosis in the Basse-Normandie area and to prevent disorders of the intestinal transit related to malabsorption, neonates then infants were given a semi-elemental hypercaloric diet, with supplements in nitrogen, MCT, minerals, vitamins and low in LCT. Diets were adjusted every month during a consultation using clinical and biological parameters. Results in the first 14 children showed that clinically as well as biologically, these children may remain within the normal range, avoiding the previously reported growth retardation and mineral or vitamin deficiencies. This procedure should allow an improvement in the quality of life and prognosis of such children, by maintaining adequate nutritional status.
在诺曼底地区进行的一项针对囊性纤维化的系统性新生儿筛查中，为预防与吸收不良相关的肠道转运障碍，新生儿随后的婴儿期均采用半要素高热量饮食，补充氮、中链甘油三酯、矿物质、维生素，且长链甘油三酯含量低。在每月一次的会诊中，根据临床和生物学参数调整饮食。对首批14名儿童的研究结果表明，无论在临床还是生物学方面，这些儿童都可能保持在正常范围内，避免了先前报道的生长发育迟缓以及矿物质或维生素缺乏的情况。通过维持充足的营养状况，这一程序应能改善此类儿童的生活质量和预后。
