Dyon J F, Hosatte F, Jobert J, Andrini P
Chir Pediatr. 1986;27(3):157-61.
Report of two cases of truncular dermoepidermal skin defect in newborn. The defect concerned the lateral thoracoabdominal area, on both sides of the umbilicus, jointed with a fine linear communication, and have the classical butterfly wind-like shape. Recovery was achieved by centripetal spontaneous cicatrization, only managed with protective vitamin dressing, in about 45 days. There was no clinical evidence of other anomaly. In this occasion, an exhaustive review of congenital skin defects is done. This disease is not frequent, 500 cases are published, principally in the scalp area (vertex). Thoracoabdominal localisation (10%) are symmetrical, spontaneously healing without surgery, in spite of a large defect. Skin defect of extremities (25% of cases) have also a good issue, except in case of associated congenital diseases; on the other hand scalp defects are sometimes complicated with sepsis or bleeding. Discussion emphasize the characteristics of skin defects, the possible pathological association (rare in case of thoracoabdominal defect) and pathogenic hypothesis, not yet definite at all.
新生儿躯干皮肤真皮表皮缺损两例报告。缺损位于胸腹外侧区域，在脐部两侧，由一条细微的线性连通相连，呈典型的蝴蝶翼状。通过向心自发瘢痕形成实现愈合，仅使用保护性维生素敷料处理，约45天愈合。无其他异常的临床证据。在此，对先天性皮肤缺损进行了详尽综述。这种疾病并不常见，已发表500例，主要位于头皮区域（头顶）。胸腹定位（10%）是对称的，尽管缺损较大，但可自发愈合无需手术。四肢皮肤缺损（25%的病例）也有较好的转归，除非伴有先天性疾病；另一方面，头皮缺损有时会并发败血症或出血。讨论强调了皮肤缺损的特征、可能的病理关联（胸腹缺损时罕见）以及致病假说，目前尚无定论。
