马凡综合征患者接受个性化主动脉根部支撑后的妊娠情况。
Pregnancy following personalised aortic root support in Marfan syndrome.
作者信息
Coroyannakis Christina, Tome Maite, Watt-Coote Ingrid, Cauldwell Matthew
机构信息
St George's University Hospitals NHS Foundation Trust, London, UK.
出版信息
Obstet Med. 2023 Sep;16(3):200-202. doi: 10.1177/1753495X221078447. Epub 2022 Feb 11.
Abstract
Marfan syndrome (MFS) is linked with adverse pregnancy events, one of the most significant being aortic dissection. We present a case of a woman with MFS with prior aortic root dilatation who opted for a Personalised External Aortic Root Support (PEARS). To date, she is only the fifth woman to have had this valve-sparing procedure prior to pregnancy. We outline her care in a tertiary centre with multidisciplinary expertise, from preconception through to the postpartum period.
摘要
马凡综合征（MFS）与不良妊娠事件有关，其中最严重的一种是主动脉夹层。我们报告一例患有马凡综合征且既往有主动脉根部扩张的女性病例，该患者选择了个性化体外主动脉根部支撑（PEARS）。迄今为止，她是第五位在怀孕前接受这种保留瓣膜手术的女性。我们概述了她在一家拥有多学科专业知识的三级中心从孕前到产后的治疗情况。
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