Tosunoğlu Bünyamin, Sena Dilek Sıddıka, Emektar Ümmühanı, Kurtuluş Yoldaş Tahir
Ankara Education and Research Hospital, Department of Neurology, Ankara, Turkey.
Acta Med Litu. 2022;29(2):171-175. doi: 10.15388/Amed.2022.29.2.3. Epub 2022 Jun 29.
Creutzfeldt-Jakob disease (CJD) is a rare, progressive, and fatal prion disease. Often the first sign of CJD is rapidly progressive dementia, leading to memory loss, personality changes, and hallucinations. Myoclonus typically occurs in 90% of cases, but often may not be an initial symptom. Other frequently occurring psychiatric symptoms include depression, anxiety, paranoia, obsessive-compulsive symptoms, and psychosis. Speech disorder, loss of balance and coordination may also accompany. We present a case of CJD with sudden onset of right hemiparesis.
克雅氏病(CJD)是一种罕见的、进行性的致命性朊病毒病。克雅氏病的首个症状通常是快速进展的痴呆,导致记忆力丧失、性格改变和幻觉。肌阵挛在90%的病例中通常会出现,但往往并非初始症状。其他常见的精神症状包括抑郁、焦虑、偏执、强迫症状和精神病。还可能伴有言语障碍、平衡和协调能力丧失。我们报告一例以右侧偏瘫急性起病的克雅氏病病例。