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一例被误诊为甲状腺功能亢进性心脏病的病例:未闭冠状静脉窦综合征合并严重三尖瓣反流的手术修复。

A case misdiagnosed as hyperthyroid heart disease: Surgical repair of unroofed coronary sinus syndrome with severe tricuspid regurgitation.

作者信息

Ding Xuejiao, Liao Zhimin, Tao Yichao, Wu Xiaofeng

机构信息

Department of Ultrasound Imaging, Xiaogan Hospital Affiliated to Wuhan University of Science and Technology, Xiaogan Central Hospital Xiaogan China.

Department of Cardiothoracic Surgery Xiaogan Hospital Affiliated to Wuhan University of Science and Technology, Xiaogan Central Hospital Xiaogan China.

出版信息

Clin Case Rep. 2023 Sep 28;11(10):e7990. doi: 10.1002/ccr3.7990. eCollection 2023 Oct.

DOI:10.1002/ccr3.7990
PMID:37780931
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC10539682/
Abstract

Unroofed coronary sinus syndrome (URCS), also known as coronary sinus septal defect, is a rare congenital heart disease. Because of its special anatomy and the lack of typical clinical symptoms, the disease is easily missed and misdiagnosed. This case report particularly describes a middle-aged male patient with URCS misdiagnosed for more than 19 years, covered by hyperthyroid heart disease, who subsequently developed uncontrollable symptoms such as chest tightness and shortness of breath and came to our hospital. After a clear diagnosis in our hospital, the patient was successfully cured after treatment with coronary sinus repair and tricuspid valvuloplasty under extracorporeal circulation.

摘要

无顶冠状静脉窦综合征(URCS),又称冠状静脉窦间隔缺损,是一种罕见的先天性心脏病。由于其特殊的解剖结构及缺乏典型临床症状,该病易被漏诊和误诊。本病例报告详细描述了一名中年男性患者,患有URCS却被误诊为甲亢性心脏病长达19年以上,随后出现胸闷、气短等无法控制的症状,遂来我院就诊。在我院明确诊断后,患者在体外循环下行冠状静脉窦修复及三尖瓣成形术,术后成功治愈。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a987/10539682/5cf6d3871b6e/CCR3-11-e7990-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a987/10539682/f96316a9748f/CCR3-11-e7990-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a987/10539682/a3a209076956/CCR3-11-e7990-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a987/10539682/5cf6d3871b6e/CCR3-11-e7990-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a987/10539682/f96316a9748f/CCR3-11-e7990-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a987/10539682/a3a209076956/CCR3-11-e7990-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a987/10539682/5cf6d3871b6e/CCR3-11-e7990-g001.jpg

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本文引用的文献

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2
Evaluation of Unroofed Coronary Sinus Syndrome Using Cardiovascular CT Angiography: An Observational Study.应用心血管 CT 血管造影术评估冠状窦未闭综合征:一项观察性研究。
AJR Am J Roentgenol. 2018 Aug;211(2):314-320. doi: 10.2214/AJR.17.19128. Epub 2018 Jun 27.
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Unroofed Coronary Sinus Syndrome: An Easily Corrected Congenital Anomaly But More Diagnostic Suspicion Is Needed.
无顶冠状静脉窦综合征:一种易于纠正的先天性异常,但需要更多的诊断怀疑。
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