Department of Pathology, Sanjay Gandhi Post-Graduate Institute Of Medical Sciences, Lucknow, Uttar Pradesh, India.
Department of Radiodiagnosis, Sanjay Gandhi Post-Graduate Institute Of Medical Sciences, Lucknow, Uttar Pradesh, India.
J Cancer Res Ther. 2023 Jul-Sep;19(5):1468-1470. doi: 10.4103/jcrt.jcrt_432_21.
The differential diagnosis for an abdominal mass in a 2-year-old child is broad and includes lesions of renal, hepatic, gastrointestinal, adrenal, and lymphatic origins. Of these, Wilms' tumor and neuroblastoma are the most common tumors, where Wilms' tumor represents about 92% of renal masses in children. Non-Wilms' renal tumors, rhabdoid tumors, and clear cell sarcoma of the kidney (CCSK) are uncommon. CCSK constitutes approximately 3% of all malignant renal tumors in childhood. In this report, we present a child presenting with a huge renal mass consistent with Wilms' tumor on computed tomography and initial biopsy. However, the final pathologic diagnosis after resection revealed CCSK.
对于 2 岁儿童的腹部肿块，鉴别诊断范围很广，包括肾脏、肝脏、胃肠道、肾上腺和淋巴来源的病变。在这些病变中，Wilms 瘤和神经母细胞瘤是最常见的肿瘤，其中 Wilms 瘤占儿童肾脏肿块的 92%左右。非 Wilms 肾肿瘤、横纹肌样瘤和肾透明细胞肉瘤（CCSK）则较为少见。CCSK 约占儿童所有恶性肾肿瘤的 3%。在本报告中，我们介绍了一名患儿，其计算机断层扫描和初次活检提示为巨大的Wilms 瘤样肾肿块。然而，切除后的最终病理诊断为 CCSK。
