Fiona Stanley Hospital, Murdoch, Western Australia, Australia
Fiona Stanley Hospital, Murdoch, Western Australia, Australia.
BMJ Case Rep. 2023 Oct 4;16(10):e254103. doi: 10.1136/bcr-2022-254103.
Discrete central endovascular pulmonary arterial lesions raise clinical concern for malignancy such as primary pulmonary artery sarcoma. We present a case of a female in her late teens who had an obstructive mid right pulmonary artery lesion found on follow-up imaging 15 years after Tetralogy of Fallot repair. The lesion was in the vicinity of a previously ligated Blalock-Taussig shunt and causing right PA stenosis with delayed perfusion to the right lung, and a flow-related distal left PA aneurysm. The lesion was excised and confirmed histologically to be inflammatory in nature. Intraoperative microbiology demonstrated growth of the Kytococcus species, and she was managed with 6 weeks of intravenous antibiotics, with a full recovery.
离散的中央血管内肺动脉病变引起临床对恶性肿瘤的关注，如原发性肺动脉肉瘤。我们报告了一个 15 年前法洛四联症修复后随访影像发现右中肺动脉阻塞性病变的女性病例。病变位于先前结扎的 Blalock-Taussig 分流器附近，导致右肺动脉狭窄，右肺灌注延迟，并伴有左肺动脉远端与血流相关的动脉瘤。病变被切除，并通过组织学证实为炎症性质。术中微生物学显示出 Kytococcus 物种的生长，她接受了 6 周的静脉抗生素治疗，完全康复。
