Subramony S H, Wee A S, Mishra S K
Muscle Nerve. 1986 Oct;9(8):700-3. doi: 10.1002/mus.880090804.
The nosologic distinction between paramyotonia congenita and hyperkalemic periodic paralysis is somewhat blurred. Muscle membrane inexcitability induced by cooling seems to be characteristic of paramyotonia congenita. The effect of cooling on the maximal compound muscle action potential (CMAP) in patients with paramyotonia congenita was compared to that in patients with hyperkalemic periodic paralysis. Diminution in CMAP amplitude and area, which was observed in paramyotonia congenita, did not occur in hyperkalemic periodic paralysis. We suggest that this effect of cooling on the CMAP can be utilized in the differentiation of these two syndromes.
先天性副肌强直和高钾性周期性瘫痪之间的疾病分类区别有些模糊。冷却诱发的肌肉膜兴奋性降低似乎是先天性副肌强直的特征。将冷却对先天性副肌强直患者最大复合肌肉动作电位（CMAP）的影响与高钾性周期性瘫痪患者的进行了比较。在先天性副肌强直中观察到的CMAP幅度和面积减小，在高钾性周期性瘫痪中并未出现。我们认为冷却对CMAP的这种影响可用于这两种综合征的鉴别。
