Pompeo Edoardo, Gagliardi Filippo, Medone Marzia, Roncelli Francesca, De Domenico Pierfrancesco, Snider Silvia, Terreni Mariarosa, Mortini Pietro
Department of Neurosurgery and Gamma Knife Radiosurgery, San Raffaele Scientific Institute, Vita-Salute University, Milan, Italy.
Department of Pathology, San Raffaele Scientific Institute, Vita-Salute University, Milan, Italy.
J Craniovertebr Junction Spine. 2023 Jul-Sep;14(3):306-310. doi: 10.4103/jcvjs.jcvjs_65_23. Epub 2023 Sep 18.
Extraskeletal chondromas (EC) are uncommon, benign cartilaginous tumours. Most common locations are upper and lower extremities. Location in the neck is extremely rare and reported only within the anterior compartment. Data are limited to just four case reports in the paediatric population. The first case of EC in neck's posterior compartment is described herein. EC present peculiar features on imaging. Aetiology is unclear; however, trauma has been suggested as possible causative mechanism. Treatment of choice is surgical excision; recurrence is not uncommon, but additional removal seems to be resolutive. All cases in literature were asymptomatic, except for one presenting respiratory stridor. The present patient suffered from neck functional limitation and upper limb hypoesthesia. Symptoms improved after surgery in both cases. Imaging follow-up at 6 months in the present case showed no sign of recurrence. ECs are rare, benign lesions. However, they may be preoperatively misinterpreted as more malignant counterparts (both radiologically or histologically), so accurate diagnostic work-up and planning of the surgical procedure are essential.
骨外软骨瘤(EC)是一种罕见的良性软骨肿瘤。最常见的部位是上肢和下肢。颈部的骨外软骨瘤极为罕见,仅在前侧肌间隙有病例报道。儿科人群中仅有4例病例报告。本文描述了首例发生在颈部后侧肌间隙的骨外软骨瘤。骨外软骨瘤在影像学上具有独特特征。病因尚不清楚;然而,创伤被认为是可能的致病机制。治疗的选择是手术切除;复发并不少见,但再次切除似乎有效。文献中的所有病例均无症状,仅有1例出现呼吸性喘鸣。本病例患者存在颈部功能受限和上肢感觉减退。两例患者术后症状均有改善。本病例6个月的影像学随访未显示复发迹象。骨外软骨瘤是罕见的良性病变。然而,它们术前可能在放射学或组织学上被误诊为恶性程度更高的肿瘤,因此准确的诊断检查和手术方案规划至关重要。