Department of Anesthesiology, Kyoto Prefectural University of Medicine, Kyoto, 602-8566, Japan.
J Med Case Rep. 2023 Nov 1;17(1):453. doi: 10.1186/s13256-023-04190-8.
The incidence of congenital complete atrioventricular block is estimated to be 1 per 20,000 deliveries. In the fetal period, the fetal mortality rate is high, but the treatment strategy has not yet been established. In severe cases, early postnatal pacing therapy is necessary.
A 0-day-old Japanese baby girl was diagnosed with fetal congenital complete atrioventricular block during a prenatal physical examination. A joint conference was held preoperatively among multidisciplinary departments, and a cesarean section was performed at 37 weeks pregnancy, immediately followed by scheduled internal ventricular pacing lead implantation in an adjacent room. Percutaneous pacing was ineffective. The epicardial pacing lead was sutured at 17.5 minutes after birth, and perioperative management was successful with a heart rate and pulse rate of 150 beats per minute.
The infant with a congenital complete atrioventricular block was rescued by an uneventful epicardial lead implantation.
先天性完全性房室传导阻滞的发病率估计为每 20000 例分娩 1 例。在胎儿期，胎儿死亡率较高，但尚未确定治疗策略。在严重的情况下，需要早期进行产后起搏治疗。
一名 0 天的日本女婴在产前体检中被诊断为胎儿先天性完全性房室传导阻滞。多学科部门术前举行了联席会议，并在 37 周妊娠时进行了剖宫产，随后立即在相邻房间进行计划中的心室内部起搏导线植入。经皮起搏无效。出生后 17.5 分钟缝合心外膜起搏导线，心率和脉搏率为 150 次/分钟，手术期间管理成功。
先天性完全性房室传导阻滞的婴儿通过顺利的心外膜导线植入得以抢救。
