Department of Orthopedics, Fujian Medical University Union Hospital, Fuzhou, China.
Department of Neurology, Fujian Medical University Union Hospital, Fuzhou, China.
Stem Cell Res. 2024 Feb;74:103268. doi: 10.1016/j.scr.2023.103268. Epub 2023 Dec 1.
The human iPS cell line, hiPS-RTT (FJMUi002-A), is derived from peripheral blood mononuclear cells (PBMCs) from a 12-year-old female RTT patient carrying a heterozygous p. R133C (c.397C > T) mutation in the MeCP2 gene. The hiPS-RTT cell line was generated by non-integrative reprogramming vectors encoding OCT3/4, SOX2, KLF4, and c-MYC and was free of genomically integrated reprogramming genes. The hiPS-RTT cell line had a normal karyotype, expressed pluripotency markers, and had capacity to form three germ layers in vitro and in vivo, which offering a useful resource to study the pathogenesis and treatment strategies of RTT.
人诱导多能干细胞系 hiPS-RTT(FJMUi002-A)源自一名 12 岁女性 RTT 患者外周血单个核细胞(PBMCs),该患者携带 MeCP2 基因中 p.R133C(c.397C>T)杂合突变。hiPS-RTT 细胞系通过非整合重编程载体编码 OCT3/4、SOX2、KLF4 和 c-MYC 生成,并且不含基因组整合的重编程基因。hiPS-RTT 细胞系具有正常的核型,表达多能性标志物,并且具有体外和体内形成三个胚层的能力,为研究 RTT 的发病机制和治疗策略提供了有用的资源。