Duan XiaoHan, Wang QingSen, Wang Ting, Sun BaoChun, Yang ShiMing, Zou YiHui
Senior Department of Otolaryngology-Head and Neck Surgery, The Sixth Medical Center of PLA General Hospital, Beijing, China.
National Clinical Research Center for Otolaryngologic Diseases, Beijing, China.
Acta Otolaryngol. 2023 Nov;143(sup1):S25-S29. doi: 10.1080/00016489.2023.2271087. Epub 2024 Feb 13.
There is no study on the hearing features of congenital malformation of middle and outer ears (CMMOE), including classification, grades, and frequency characteristics, which play a decisive role in the selection of precise hearing solutions for patients. To analyze the hearing features of CMMOE and provide guidance for clinical practice. 298 cases (351 ears) with CMMOE were retrospectively analyzed for the features of 0.5 ∼ 4KHz pure tone hearing, including the classification, grades and frequency characteristics. We observed conductive deafness in 84.3% (296/351), mixed deafness in 15.7% (55/351), and 0% (0/351) sensorineural deafness. Grades measured by average Air Conduction Thresholds (ACT) of pure tone: Mild deafness (26-40dB HL) 0.6% (2/351), moderate deafness (41-55dB HL) 10.3% (36/351), moderate to severe deafness (56-70dB HL) 46.1%(162/351), severe deafness (71-90dB HL) 39.9%(140/351), extremely severe deafness (> 90 dB HL) 3.1%(11/351). The average ACT of 296 ears conductive deafness was 67 ± 10 dB HL, of which 56-80dB HL accounted for 78.1% (274/351). In 55 ears with mixed deafness, 32 ears (32/55 = 58.2%) increased Bone Conduction Threshold (BCT) at a single frequency, and out of 32 ears, 31ears (31/55 = 56.4%) ≤40dB HL, 25(25/32 = 78.1%) ears at 2KHz. In 55 ears with mixed deafness, 87.3% (48/55) increased BCT at 2KHz, and the average BCT was 35 ± 10dB HL. CMMOE result mainly in conductive deafness, moderate to severe and severe deafness. In mixed deafness, the BCT increased mainly at a single frequency, 2KHz and ≤40dB HL. These data suggest that bone-conductive hearing devices are a good solution for CMMOE hearing impairment.
目前尚无关于中耳和外耳先天性畸形（CMMOE）听力特征的研究，包括分类、分级及频率特征等，而这些特征对于为患者选择精确的听力解决方案起着决定性作用。为分析CMMOE的听力特征并为临床实践提供指导，对298例（351耳）CMMOE患者的0.5～4kHz纯音听力特征进行回顾性分析，包括分类、分级及频率特征。我们观察到84.3%（296/351）为传导性聋，15.7%（55/351）为混合性聋，感音神经性聋为0%（0/351）。通过纯音平均气导阈值（ACT）测量分级：轻度聋（26 - 40dB HL）0.6%（2/351），中度聋（41 - 55dB HL）10.3%（36/351），中重度聋（56 - 70dB HL）46.1%（162/351），重度聋（71 - 90dB HL）39.9%（140/351），极重度聋（>90dB HL）3.1%（11/351）。296耳传导性聋的平均ACT为67±10dB HL，其中56 - 80dB HL占78.1%（274/351）。在55耳混合性聋中，32耳（32/55 = 58.2%）单频骨导阈值（BCT）升高，在这32耳中，31耳（31/55 = 56.4%）≤40dB HL，25耳（25/32 = 78.1%）在2kHz。在55耳混合性聋中，87.3%（48/55）在2kHz时BCT升高，平均BCT为35±10dB HL。CMMOE主要导致传导性聋、中重度和重度聋。在混合性聋中，BCT主要在单频升高，为2kHz且≤40dB HL。这些数据表明骨导听力装置是CMMOE听力障碍的良好解决方案。
