Division of Gastroenterology and Hepatology, Department of Medicine, Mayo Clinic, Rochester, Minnesota.
Division of Gastroenterology and Hepatology, Department of Medicine, Mayo Clinic, Rochester, Minnesota.
Cell Mol Gastroenterol Hepatol. 2024;17(4):623-638. doi: 10.1016/j.jcmgh.2023.12.010. Epub 2023 Dec 30.
Hepatobiliary cancers (HBCs) include hepatocellular carcinoma, cholangiocarcinoma, and gallbladder carcinoma, which originate from the liver, bile ducts, and gallbladder, respectively. They are responsible for a substantial burden of cancer-related deaths worldwide. Despite knowledge of risk factors and advancements in therapeutics and surgical interventions, the prognosis for most patients with HBC remains bleak. There is evidence from familial aggregation and case-control studies to suggest a familial risk component in HBC susceptibility. Recent progress in genomics research has led to the identification of germline variants including single nucleotide polymorphisms (SNPs) and pathogenic or likely pathogenic (P/LP) variants in cancer-associated genes associated with HBC risk. These findings emerged from genome-wide association studies and next-generation sequencing techniques such as whole-exome sequencing. Patients with other cancer types, including breast, colon, ovarian, prostate, and pancreatic cancer, are recommended by guidelines to undergo germline genetic testing, but similar recommendations are lagging in HBC. This prompts the question of whether multi-gene panel testing should be integrated into clinical guidelines for HBC management. Here, we review the hereditary genetics of HBC, explore studies investigating SNPs and P/LP variants in HBC patients, discuss the clinical implications and potential for personalized treatments and impact on patient's family members, and conclude that additional studies are needed to examine how genetic testing can be applied clinically.
肝胆癌(HBC)包括肝细胞癌、胆管癌和胆囊癌,分别源自肝脏、胆管和胆囊。它们在全球范围内导致了大量的癌症相关死亡。尽管人们了解了风险因素,并在治疗和手术干预方面取得了进展,但大多数 HBC 患者的预后仍然不容乐观。有家族聚集和病例对照研究的证据表明,HBC 易感性存在家族风险因素。基因组学研究的最新进展导致确定了与 HBC 风险相关的癌症相关基因中的种系变体,包括单核苷酸多态性(SNPs)和致病性或可能致病性(P/LP)变体。这些发现来自全基因组关联研究和下一代测序技术,如外显子组测序。指南建议其他癌症类型(包括乳腺癌、结肠癌、卵巢癌、前列腺癌和胰腺癌)的患者进行种系基因检测,但在 HBC 中类似的建议却滞后。这就提出了一个问题,即多基因面板检测是否应该纳入 HBC 管理的临床指南。在这里,我们回顾了 HBC 的遗传性遗传学,探讨了研究 HBC 患者 SNPs 和 P/LP 变体的研究,讨论了其临床意义和个性化治疗的潜力及其对患者家属的影响,并得出结论,需要进一步研究如何将基因检测应用于临床。