在一名等待法洛四联症初次修复手术的72岁患者中使用丙吡胺治疗法洛四联症发作。
Treating Tet Spells With Disopyramide in a 72-Year-Old Awaiting Primary Repair of Tetralogy of Fallot.
作者信息
Kalapurakal George T, Monaco James M
机构信息
Department of Cardiology, Advanced Heart Failure, Advocate Christ Medical Center, Chicago, Illinois, USA.
出版信息
JACC Case Rep. 2023 Nov 3;28:102093. doi: 10.1016/j.jaccas.2023.102093. eCollection 2023 Dec 20.
Abstract
An adult with unrepaired tetralogy of Fallot presented with frequent tet spells. Her course was complicated by severe cyanotic spells and tachycardia-bradycardia syndrome that limited beta blocker use to stabilize her spells. She markedly improved after disopyramide initiation and underwent successful tetralogy of Fallot repair with excellent functional outcome.
摘要
一名患有未经修复的法洛四联症的成年人频繁出现缺氧发作。她的病情因严重的青紫发作和心动过速-心动过缓综合征而复杂化，这限制了β受体阻滞剂的使用以稳定发作。在开始使用丙吡胺后，她的病情明显改善，并成功接受了法洛四联症修复手术，功能预后良好。
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