Department of Surgery, College of Medicine and Health Sciences, University of Gondar, Gondar, Ethiopia.
J Med Case Rep. 2024 Jan 16;18(1):19. doi: 10.1186/s13256-023-04328-8.
Agenesis of the right hepatic lobe is a rare congenital anomaly. Developmental anomalies of the right lobe of the liver were first reported in 1870 by Heller [6]. Anatomical variations of the liver are common, occur during the normal development of the organ, and correspond to variations in the distribution of liver territories. Agenesis of the right lobe of the liver is an incidental finding revealed by the popularization of ultrasonography, computed tomography, or magnetic resonance imaging due to the condition being asymptomatic.
A 35-year-old Ethiopian female patient presented to the outpatient clinic with a complaint of right upper abdominal pain for 1 year, along with symptoms of fatty meal intolerance and long-standing epigastric burning pain. Her examination was unremarkable, and imaging investigations were suggestive of right hepatic lobe agenesis with multiple gallstones. Therefore, the patient was operated on and discharged with no perioperative complications.
Surgical understanding of such anatomical anomalies is necessary for surgical planning, the appropriate interpretation of intraoperative surgical findings, and the design of postoperative therapy. Here we report a case of right hepatic lobe agenesis with cholelithiasis and cholidocholithiasis and a brief review of right lobe agenesis in the literature.
右肝叶发育不全是一种罕见的先天性异常。1870 年,Heller [6]首次报道了右肝叶的发育异常。肝脏的解剖变异很常见,发生在器官的正常发育过程中,与肝区分布的变异相对应。由于无症状,右肝叶发育不全是超声、计算机断层扫描或磁共振成像普及后偶然发现的。
一位 35 岁的埃塞俄比亚女性患者因右上腹痛 1 年,伴有脂肪餐不耐受和长期上腹痛就诊于门诊。她的检查无明显异常,影像学检查提示右肝叶发育不全伴多发性胆囊结石。因此,患者接受了手术治疗,术后无围手术期并发症出院。
手术医生需要了解这些解剖异常,以便进行手术规划、正确解读术中手术发现,并设计术后治疗方案。在此,我们报告一例右肝叶发育不全伴胆石症和胆总管结石,并对文献中的右肝叶发育不全进行了简要回顾。