Singla Kunal, Goyal Nishant, Mittal Pulkit, Qamer Zahed Ali, Chaturvedi Jitender, Kumar Arvind
Department of Neurosurgery, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, India.
Department of Pathology, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, India.
Surg Neurol Int. 2024 Jan 5;15:1. doi: 10.25259/SNI_201_2023. eCollection 2024.
FD is relatively rare in the craniofacial region, accounting for only 20% of all cases. Currently, two general subtypes of FD are recognized: monostotic and polyostotic. The monostotic form is more frequent, accounting for 75% to 80% of fibrous dysplasia cases.
An 18-year-old male presented with the complaint of bony-hard swelling over the forehead for 8 years. Radiology showed an expansile osseous lesion involving frontal bones. The patient underwent bi-frontal craniectomy with gross total resection of tumour mass with titanium mesh cranioplasty. His postoperative period was uneventful and was discharged on the seventh postoperative day.
The cases of monostotic skull fibrous dysplasia should be treated by resection of the affected bone and cranioplasty. However, a more conservative re-contouring may be carried out in cases with multifocal involvement or when the excision is considered risky due to proximity to the major venous sinuses.
骨纤维异常增殖症（FD）在颅面部相对少见，仅占所有病例的20%。目前，FD公认有两种主要亚型：单骨型和多骨型。单骨型更为常见，占骨纤维异常增殖症病例的75%至80%。
一名18岁男性主诉前额部硬性肿胀8年。影像学检查显示额骨有一膨胀性骨质病变。患者接受了双侧额部颅骨切除术，肿瘤块全切，并进行了钛网颅骨成形术。术后恢复顺利，术后第七天出院。
单骨型颅骨骨纤维异常增殖症病例应通过切除受累骨并进行颅骨成形术治疗。然而，对于多灶性受累病例或因靠近主要静脉窦而认为切除有风险的病例，可采用更保守的重塑手术。
