Hong Inseok, Kang Dong Cheol, Leem Dae-Ho, Baek Jin-A, Ko Seung-O
Department of Oral and Maxillofacial Surgery, School of Dentistry, Chonbuk National University Dental Hospital, 20, Geonji-ro, Deokjin-gu, Jeonju-si, Jeollabuk-do Republic of Korea.
Research Institute of Clinical Medicine-Biomedical Research Institute, Chonbuk National University Hospital, 20, Geonji-ro, Deokjin-gu, Jeonju-si, Jeollabuk-do Republic of Korea.
Maxillofac Plast Reconstr Surg. 2020 Sep 16;42(1):31. doi: 10.1186/s40902-020-00275-2. eCollection 2020 Dec.
Fibrous dysplasia (FD) is a rare, sporadic, and benign congenital condition in which normal cancellous bone is replaced by fibro-osseous tissue with immature osteogenesis. FD localized in the cranial and facial bones is called craniofacial fibrous dysplasia (CFD). Cystic degeneration in CFD cases is rare; cystic degeneration appearing in both the maxilla and the mandible FD lesion is even rarer. The aim of this article was to report a case of fibrous dysplasia of the mandible and maxilla complicated by nonspecific cystic degeneration.
A 30-year-old woman presented with a rare case of non-specific cystic degeneration in a mandible and maxilla FD lesion that occurred 11 years after surgery. She was diagnosed with polyostotic CFD and underwent maxillary and mandibular bone contouring. Cyst enucleation under general anesthesia was performed in the mandibular region due to pain and discomfort.
In cases involving non-aggressive and non-invasive FD cystic degeneration in focal areas, conservative treatment is recommended. However, if cystic degeneration of FD develops rapidly and causes discomfort, pain, or dysfunction, surgical treatment should be considered.
骨纤维异常增殖症（FD）是一种罕见的、散发性的先天性良性疾病，正常的松质骨被成骨不成熟的纤维骨组织所替代。局限于颅骨和面部骨骼的FD称为颅面部骨纤维异常增殖症（CFD）。CFD病例中的囊性变罕见；上颌骨和下颌骨FD病变均出现囊性变则更为罕见。本文旨在报告1例下颌骨和上颌骨骨纤维异常增殖症合并非特异性囊性变的病例。
一名30岁女性，术后11年出现罕见的下颌骨和上颌骨FD病变非特异性囊性变。她被诊断为多骨型CFD，并接受了上颌骨和下颌骨轮廓整形手术。由于疼痛和不适，在全身麻醉下对下颌区域进行了囊肿摘除术。
对于局部非侵袭性和非侵入性FD囊性变的病例，建议采取保守治疗。然而，如果FD的囊性变迅速发展并引起不适、疼痛或功能障碍，则应考虑手术治疗。
