Department of Thoracic and Cardiovascular Surgery, Heart and Diabetes Center North Rhine- Westphalia, University Hospital Ruhr-University Bochum, Bad Oeynhausen, Germany.
Institute of Radiology, Nuclear Medicine and Molecular Imaging, Heart and Diabetes Center North Rhine-Westphalia, University Hospital Ruhr-University Bochum, Bad Oeynhausen, Germany.
J Cardiothorac Surg. 2024 Feb 22;19(1):105. doi: 10.1186/s13019-024-02529-w.
Midventricular hypertrophic obstructive cardiomyopathy (HOCM) is characterized by hypertrophy of the interventricular septum (IVS) and - in rare cases - of the papillary muscles (PM), which subsequently can cause dynamic left ventricular outflow tract obstruction (LVOTO) and severe heart failure symptoms. We report on a rare case of a 44-year-old patient suffering from midventricular HOCM with hypertrophic anterolateral PM and an additional chorda between the PM and the IVS.We describe a new surgical approach via right anterolateral thoracotomy in 3-dimensional (3D) video-assisted minimal-invasive technique with resection of hypertrophic PMs as well as the entire mitral valve-apparatus and valve replacement avoiding septal myectomy and potentially associated complications. After an uneventful procedure clinical symptoms improved from NYHA III-IV at baseline to NYHA 0-I postoperatively and remained stable over a follow-up period of 24 months. Therefore, the presented technique may be considered as a new and alternative approach in patients with hypertrophic PMs and hypertrophic IVS as subtype of midventricular HOCM.
室间隔中部肥厚型梗阻性心肌病(HOCM)的特征是室间隔(IVS)肥厚,在极少数情况下,乳头肌(PM)也会肥厚,从而导致左心室流出道梗阻(LVOTO)和严重的心力衰竭症状。我们报告了一例罕见的 44 岁患者,患有室间隔中部肥厚型梗阻性心肌病,伴有肥厚的前外侧乳头肌,以及乳头肌和 IVS 之间的额外腱索。我们描述了一种新的手术方法,通过右侧前外侧开胸术在 3 维(3D)视频辅助微创技术下进行,切除肥厚的乳头肌以及整个二尖瓣装置,并进行瓣膜置换,避免进行室间隔切除术和潜在的相关并发症。在手术过程顺利,无并发症的情况下,患者的临床症状从术前的 NYHA III-IV 级改善至术后的 NYHA 0-I 级,并在 24 个月的随访期间保持稳定。因此,对于肥厚性乳头肌和肥厚性 IVS 作为室间隔中部肥厚型梗阻性心肌病亚型的患者,该技术可被视为一种新的替代方法。