Jain Avani, Meher Ravi, Khurana Nita
Department of ENT, ESIC Medical College and Hospital, Faridabad, India.
Department of ENT, Maulana Azad Medical College, New Delhi, India.
Indian J Otolaryngol Head Neck Surg. 2024 Feb;76(1):1075-1079. doi: 10.1007/s12070-023-04120-6. Epub 2023 Aug 10.
Paediatric rhabdomyosarcoma most commonly occurs in the head and neck region. Its treatment is complex, including multi-drug chemotherapy, surgery and radiotherapy. Here, we report a case of alveolar rhabdomyosarcoma of the temporal region with a metastatic cervical lymph node, in a 15-year-old girl, and its management. The patient received ne-adjuvant chemotherapy, followed by surgery and post operative radiotherapy. Literature was also reviewed for the various treatment modalities for these rare tumours. Rhabdomyosarcoma of the temporal region has rarely been reported in the literature. Due to the rarity of these tumours, there are difficulties in creating standardized therapeutic protocols. However, multimodality treatment, including chemotherapy, surgery and radiotherapy, has been shown to improve the overall survival rate.
小儿横纹肌肉瘤最常发生于头颈部区域。其治疗复杂,包括多药化疗、手术及放疗。在此,我们报告一例15岁女孩颞部肺泡状横纹肌肉瘤伴颈部转移性淋巴结及其治疗情况。该患者接受了新辅助化疗,随后进行手术及术后放疗。我们还查阅了文献中关于这些罕见肿瘤的各种治疗方式。颞部横纹肌肉瘤在文献中鲜有报道。由于这些肿瘤罕见,制定标准化治疗方案存在困难。然而,包括化疗、手术及放疗在内的多模式治疗已显示可提高总生存率。