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抗阻训练对轻度和重度肌肉营养不良小鼠肌肉功能的有益影响可作为杜氏肌营养不良症的临床前选择。

Beneficial effects of resistance training on both mild and severe mouse dystrophic muscle function as a preclinical option for Duchenne muscular dystrophy.

机构信息

Sorbonne Université, Institut de Biologie Paris-Seine, UMR CNRS 8256, INSERM ERL U1164, Biological Adaptation and Ageing, Paris, F-75013 France.

Sorbonne Université, INSERM, Institut de Myologie, Centre de Recherche en Myologie, F-75013 Paris, France.

出版信息

PLoS One. 2024 Mar 8;19(3):e0295700. doi: 10.1371/journal.pone.0295700. eCollection 2024.

DOI:10.1371/journal.pone.0295700
PMID:38457407
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC10923407/
Abstract

Mechanical overloading (OVL) resulting from the ablation of muscle agonists, a supra-physiological model of resistance training, reduces skeletal muscle fragility, i.e. the immediate maximal force drop following lengthening contractions, and increases maximal force production, in mdx mice, a murine model of Duchene muscular dystrophy (DMD). Here, we further analyzed these beneficial effects of OVL by determining whether they were blocked by cyclosporin, an inhibitor of the calcineurin pathway, and whether there were also observed in the D2-mdx mice, a more severe murine DMD model. We found that cyclosporin did not block the beneficial effect of 1-month OVL on plantaris muscle fragility in mdx mice, nor did it limit the increases in maximal force and muscle weight (an index of hypertrophy). Fragility and maximal force were also ameliorated by OVL in the plantaris muscle of D2-mdx mice. In addition, OVL increased the expression of utrophin, cytoplamic γ-actin, MyoD, and p-Akt in the D2-mdx mice, proteins playing an important role in fragility, maximal force gain and muscle growth. In conclusion, OVL reduced fragility and increased maximal force in the more frequently used mild mdx model but also in D2-mdx mice, a severe model of DMD, closer to human physiopathology. Moreover, these beneficial effects of OVL did not seem to be related to the activation of the calcineurin pathway. Thus, this preclinical study suggests that resistance training could have a potential benefit in the improvement of the quality of life of DMD patients.

摘要

肌肉激动剂消融导致的机械性过载(OVL),一种超生理的抗阻训练模型,可降低骨骼肌脆弱性,即在拉长收缩后即刻最大力下降,并增加 mdx 小鼠(杜氏肌营养不良症的一种鼠模型)的最大力产生。在这里,我们通过确定 OVL 是否被钙调神经磷酸酶通路抑制剂环孢素阻断,以及 D2-mdx 小鼠(一种更严重的肌营养不良症鼠模型)是否也观察到这些有益作用,进一步分析了 OVL 的这些有益作用。我们发现,环孢素不能阻断 1 个月 OVL 对 mdx 小鼠比目鱼肌脆弱性的有益作用,也不能限制最大力和肌肉重量(肥大的指标)的增加。OVL 也改善了 D2-mdx 小鼠比目鱼肌的脆弱性和最大力。此外,OVL 增加了 D2-mdx 小鼠比目鱼肌中 utrophin、细胞质 γ-肌动蛋白、MyoD 和 p-Akt 的表达,这些蛋白在脆弱性、最大力增加和肌肉生长中发挥重要作用。总之,OVL 降低了更常用的轻度 mdx 模型中的脆弱性并增加了最大力,但也降低了 D2-mdx 小鼠(一种更接近人类病理生理学的严重肌营养不良症模型)中的脆弱性并增加了最大力。此外,OVL 的这些有益作用似乎与钙调神经磷酸酶通路的激活无关。因此,这项临床前研究表明,抗阻训练可能有益于改善 DMD 患者的生活质量。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/12a2/10923407/8eb91484b9f8/pone.0295700.g006.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/12a2/10923407/ab0383b09a3e/pone.0295700.g001.jpg
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https://cdn.ncbi.nlm.nih.gov/pmc/blobs/12a2/10923407/485a38a3528d/pone.0295700.g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/12a2/10923407/d8e6fa67969f/pone.0295700.g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/12a2/10923407/8eb91484b9f8/pone.0295700.g006.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/12a2/10923407/ab0383b09a3e/pone.0295700.g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/12a2/10923407/124b867784ca/pone.0295700.g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/12a2/10923407/a082871f5bb5/pone.0295700.g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/12a2/10923407/485a38a3528d/pone.0295700.g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/12a2/10923407/d8e6fa67969f/pone.0295700.g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/12a2/10923407/8eb91484b9f8/pone.0295700.g006.jpg

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