Department of Clinical Laboratory, Shengli Oilfield Central Hospital, 257034 Dongying, Shandong, China.
Department of Respiratory and Critical Care Medicine, Shengli Oilfield Central Hospital, 257034 Dongying, Shandong, China.
Ann Ital Chir. 2024;95(1):6-12.
Adenoid cystic carcinoma (ACC) is a malignant tumor originating in the salivary glands. It most commonly affects the salivary and lacrimal glands, with less frequent occurrences in the esophagus. Esophageal ACC (EACC) typically manifests in the middle or lower parts of the esophagus, with exceedingly rare instances in the upper part. Lung metastasis in EACC is uncommon, and understanding its clinical features and treatment strategies remains challenging. In this study, we present a case of ACC originating in the upper esophagus with lung metastasis. The patient, a middle-aged female, was admitted to the Department of Respiratory and Critical Care Medicine due to an esophageal mass discovered during physical examination that had been present for 4.5 years, along with a newly identified pulmonary nodule for 2 weeks. An X-ray barium meal revealed the presence of a benign esophageal cervical mass. Gastroscopy revealed elevated lesions below the esophageal inlet, and a pathological biopsy confirmed the diagnosis of EACC. The aim of this case report is to enhance understanding of this rare condition and improve clinicians' awareness of the disease. By providing details of the patient's diagnosis, clinical presentation, imaging features and pathological features, we aim to improve diagnostic accuracy and clinical management of similar cases in the future.
腺样囊性癌（ACC）是一种起源于唾液腺的恶性肿瘤。它最常影响唾液腺和泪腺，在食管中较少发生。食管腺样囊性癌（EACC）通常发生在食管的中部或下部，非常罕见于上部。EACC 的肺转移并不常见，了解其临床特征和治疗策略仍然具有挑战性。在本研究中，我们报告了一例起源于食管上段并伴有肺转移的 ACC 病例。该患者为中年女性，因体检时发现食管肿块 4.5 年，新发现肺部结节 2 周而入住呼吸与危重症医学科。X 射线钡餐显示颈段食管良性肿块。胃镜检查发现食管入口下方隆起性病变，病理活检证实为 EACC。本病例报告的目的是提高对这种罕见疾病的认识，并增强临床医生对该疾病的认识。通过提供患者的诊断、临床表现、影像学特征和病理特征的详细信息，我们旨在提高未来类似病例的诊断准确性和临床管理水平。
