Coelho Mogárrio Inês, Pilar Carla, Santos Ema, Alves Fátima
Pediatric Surgery, Hospital Central do Funchal, Funchal, PRT.
Cureus. 2024 Feb 19;16(2):e54454. doi: 10.7759/cureus.54454. eCollection 2024 Feb.
Splenogonadal fusion is a rare, benign congenital malformation characterized by the association of splenic tissue and gonads (typically testicles). It is a condition of male predominance and can be classified into two types: continuous, if the spleen and gonad are united by a splenic cord or fibrous tissue, or discontinuous. Splenogonadal fusion is often associated with other congenital anomalies such as cryptorchidism, limb defects, and micrognathia. Differential diagnosis can be difficult and includes inguinal hernia, spermatic cord cyst, cryptorchidism, or testicular mass. Due to little knowledge of the pathology, unnecessary orchidectomies are often performed. A previously healthy five-year-old boy was sent to a pediatric surgery appointment due to testicular asymmetry. The physical examination showed a painless, nodular mass adhering to the upper pole of the left testicle, without any palpable inguinal masses. Tumor markers were negative, and a testicular ultrasound with Doppler revealed a mass suggestive of an accessory testicle. Left inguinal surgical exploration revealed the presence of a mass joined by fibrous tissue to the upper pole of the testicle, but no connection to the native spleen was found. Total excision was performed with the testicle's preservation. The anatomopathological analysis revealed morphological aspects compatible with splenic tissue with normal characteristics. The diagnosis of splenogonadal fusion is rare and complex, requires several differential diagnoses, and is often made intraoperatively.The prognosis is excellent as long as there are no associated malformations. A high level of suspicion for this pathology, with recognition of the anatomical structures, can avoid unnecessary orchidectomy.
脾性腺融合是一种罕见的良性先天性畸形,其特征是脾组织与性腺(通常为睾丸)相连。这是一种男性占主导的病症,可分为两种类型:连续性的,即脾脏和性腺通过脾索或纤维组织相连;或非连续性的。脾性腺融合常与其他先天性异常相关,如隐睾、肢体缺陷和小颌畸形。鉴别诊断可能困难,包括腹股沟疝、精索囊肿、隐睾或睾丸肿物。由于对该病理了解甚少,常进行不必要的睾丸切除术。一名此前健康的5岁男孩因睾丸不对称被送去小儿外科就诊。体格检查显示左侧睾丸上极附着一个无痛性结节状肿物,腹股沟未触及肿物。肿瘤标志物为阴性,睾丸多普勒超声显示一个肿物,提示副睾。左侧腹股沟手术探查发现一个肿物通过纤维组织与睾丸上极相连,但未发现与脾脏相连。在保留睾丸的情况下进行了完整切除。解剖病理学分析显示形态学特征与正常脾组织相符。脾性腺融合的诊断罕见且复杂,需要进行多种鉴别诊断,且常于术中做出。只要没有相关畸形,预后良好。对此病理高度怀疑并识别解剖结构可避免不必要的睾丸切除术。