Gemnani Rinkle, Saboo Keyur, Patil Rajvardhan, Kumar Sunil, Acharya Sourya
Department of Medicine, Jawaharlal Nehru Medical College, Datta Meghe Institute of Higher Education and Research (Deemed to be University), Wardha, IND.
Department of Internal Medicine, Jawaharlal Nehru Medical College, Datta Meghe Institute of Higher Education and Research (Deemed to be University), Wardha, IND.
Cureus. 2024 Feb 22;16(2):e54729. doi: 10.7759/cureus.54729. eCollection 2024 Feb.
Superior vena cava syndrome (SVCS) is a collection of signs and symptoms resulting from superior vena cava obstruction which is either partial or complete. SVCS is a rare clinical entity, often associated with various malignancies. T-cell lymphoblastic lymphoma (T-LBL) primarily of the mediastinum (thymus) is a rare and aggressive non-Hodgkin lymphoma that can lead to SVCS. We discuss the case of a 19-year-old male who arrived at our emergency department with symptoms of cough, breathlessness, and facial puffiness along with swelling in the right anterior mediastinum for two weeks suggestive of acute SVCS. An anterior mediastinal mass was confirmed on a chest X-ray and computed tomography. A biopsy of the mass revealed primary mediastinal (thymic) T-LBL. This case report focuses on the unique presentation of a T-LBL as SVCS in a 19-year-old male. Moreover, it highlights the need for vigilance among healthcare providers in recognizing this atypical complication and underscores the critical importance of early diagnosis and timely intervention.
上腔静脉综合征（SVCS）是由上腔静脉部分或完全阻塞引起的一系列体征和症状。SVCS是一种罕见的临床病症，常与各种恶性肿瘤相关。主要位于纵隔（胸腺）的T细胞淋巴母细胞淋巴瘤（T-LBL）是一种罕见且侵袭性的非霍奇金淋巴瘤，可导致SVCS。我们讨论了一名19岁男性的病例，他因咳嗽、呼吸困难、面部肿胀以及右前纵隔肿胀两周而到我们急诊科就诊，提示急性SVCS。胸部X线和计算机断层扫描证实前纵隔有肿块。肿块活检显示为原发性纵隔（胸腺）T-LBL。本病例报告重点关注一名19岁男性T-LBL以SVCS形式的独特表现。此外，它强调了医疗保健提供者在识别这种非典型并发症时保持警惕的必要性，并强调了早期诊断和及时干预的至关重要性。
