Li Xi E, McElhinney Doff B, Lui George K, Clark Daniel E, Woo Jennifer P
Department of Anesthesia, Stanford University, Stanford, California.
Department of Cardiothoracic Surgery and Pediatrics (Cardiology), Stanford University, Stanford, California.
CASE (Phila). 2024 Mar 8;8(3Part A):186-192. doi: 10.1016/j.case.2023.12.006. eCollection 2024 Mar.
• SOVA is a rare cardiac anomaly. • Ruptured SOVA carries a high mortality rate. • SOVA often coexists with other congenital lesions, most commonly VSD and bicuspid AV. • Ruptured SOVA needs repair; percutaneous repair is a safe alternative to surgery. • Echo plays a vital role in both diagnosing SOVA and guiding percutaneous closure.
• 窦管交界动脉瘤(SOVA)是一种罕见的心脏异常。
• 破裂的窦管交界动脉瘤死亡率很高。
• 窦管交界动脉瘤常与其他先天性病变并存,最常见的是室间隔缺损(VSD)和二叶式主动脉瓣(bicuspid AV)。
• 破裂的窦管交界动脉瘤需要修复;经皮修复是手术的一种安全替代方法。
• 超声心动图在诊断窦管交界动脉瘤和指导经皮封堵方面都起着至关重要的作用。