Almourgi Majed A
Surgery, College of Medicine, Taif University, Taif, SAU.
Cureus. 2024 Mar 14;16(3):e56146. doi: 10.7759/cureus.56146. eCollection 2024 Mar.
Cystic lymphangioma (CL) is an uncommon congenital malformation of the lymphatic system, often occurring in the head, neck, or mediastinum, potentially causing compression symptoms like dysphagia or dyspnea, and in rare cases, neurogenic thoracic outlet syndrome (nTOS). This report details a case of a 38-year-old male with a four-year history of a left lower neck mass, experiencing tingling in his left forearm over the last six months. The examination revealed a left supraclavicular cystic mass, with imaging suggesting CL compressing neurovascular structures. The patient underwent successful complete surgical excision through a left supraclavicular approach. Histopathology confirmed CL, with no recurrence observed over 19 months. The case highlights that cervicothoracic CL with adult presentation can cause pressure symptoms including nTOS. It also underscores the role of a multimodal diagnostic approach to differentiate it from other neck masses and that a supraclavicular approach can effectively remove the cyst, especially when the lower extension is not deep and there is no surrounding inflammation, thereby leading to relieving pressure and preventing recurrence.
囊性淋巴管瘤(CL)是一种罕见的先天性淋巴系统畸形,常发生于头、颈或纵隔,可能导致吞咽困难或呼吸困难等压迫症状,在罕见情况下,可导致神经源性胸廓出口综合征(nTOS)。本报告详细介绍了一例38岁男性病例,该患者左颈部肿块已有四年病史,在过去六个月中左前臂出现刺痛。检查发现左锁骨上囊性肿块,影像学检查提示CL压迫神经血管结构。患者通过左锁骨上入路成功进行了完整的手术切除。组织病理学证实为CL,在19个月内未观察到复发。该病例强调,成人表现的颈胸段CL可引起包括nTOS在内的压迫症状。它还强调了多模式诊断方法在将其与其他颈部肿块区分开来方面的作用,以及锁骨上入路可以有效地切除囊肿,特别是当下部延伸不深且无周围炎症时,从而减轻压迫并防止复发。