Ramirez-Amoros Carla, Estefania-Fernandez Karla, Moratilla-Lapeña Lucas, Vilanova-Sanchez Alejandra, Lopez Pereira Pedro, Martinez Urrutia Maria Jose
La Paz Children's University Hospital, Department of Paediatric Surgery, Madrid, Spain.
Urol Case Rep. 2024 Apr 10;54:102736. doi: 10.1016/j.eucr.2024.102736. eCollection 2024 May.
Bladder duplication (BD) is a rare malformation that is often associated to other anomalies. We report a newborn diagnosed with BD in the sagittal plane, associated to persistent urogenital sinus (UGS), given the opening of the vagina immediately below the bladder neck. It is the fourth time this association is reported. Surgical repair was made: both bladders were joined, the common channel was left as urethra and the vagina was descended with a vaginoplasty with an intestinal segment. She also presented an anterior anus, that required posterior mobilization. The patient is currently 3 years old with good sphincter control.
膀胱重复畸形(BD)是一种罕见的畸形,常与其他异常相关。我们报告一例新生儿,在矢状面被诊断为BD,伴有持续性泌尿生殖窦(UGS),因为阴道开口紧邻膀胱颈下方。这是该关联第四次被报道。进行了手术修复:将两个膀胱连接起来,保留共同通道作为尿道,并通过肠段阴道成形术使阴道下降。她还存在前位肛门,需要进行后方游离。该患者目前3岁,括约肌控制良好。