University of Colorado School of Medicine, Aurora, CO.
Department of Visceral and Thoracic Surgery, Cantonal Hospital of Winterthur, Switzerland.
Urology. 2021 Mar;149:199-205. doi: 10.1016/j.urology.2020.11.001. Epub 2020 Nov 13.
To describe 5 cases with complete urinary bladder duplication, their associated conditions, and their respective treatment. Urinary bladder duplication is an extremely rare congenital anomaly of the urinary system. So far about 70 cases have been published in the English literature, most of them as case reports and a few case series.
All consecutive patients with bladder duplication treated at our institution between 2000 and 2015 were included. Patient records were retrospectively analyzed, and 5 patients with urinary bladder duplication were identified (see Summary Figure). Two patients were male. All duplications were recognized by health care providers. In 1 case recognition was prenatal (MRI in utero at 22 weeks of gestation), the latest recognition was at 12 months of age. A voiding cystourethrography was performed in 4 patients to confirm the diagnosis. In 4 patients the bladder duplication could be classified according to Abrahamson with 3 complete reduplications and one complete sagittal septum. All patients suffered from associated congenital diseases, but only one patient had urinary tract infections. Surgical treatment was only performed in one patient. Median follow-up was 34 months.
Urinary bladder duplications reflect extremely seldom disorders that are almost always associated with other congenital anomalies. Treatment depends on patients' symptoms and associated conditions and hence needs to be individualized to each patient.
描述 5 例完全性膀胱重复畸形患者的相关情况及其治疗方法。膀胱重复畸形是一种极其罕见的泌尿系统先天性畸形。目前，在英文文献中已报道约 70 例，其中大多数为病例报告，少数为病例系列。
本研究纳入了 2000 年至 2015 年在我院治疗的所有连续的膀胱重复畸形患者。回顾性分析患者病历，共发现 5 例膀胱重复畸形患者（见概要图）。其中 2 例为男性。所有的重复畸形均由医护人员发现。1 例在产前（妊娠 22 周时的 MRI）发现，最晚的发现时间为 12 个月。4 例患者行排尿性膀胱尿道造影以明确诊断。根据 Abrahamson 的分类，4 例患者的膀胱重复畸形可分为 3 例完全性重复和 1 例完全性矢状隔。所有患者均患有其他先天性疾病，但仅 1 例患者发生过尿路感染。仅 1 例患者接受了手术治疗。中位随访时间为 34 个月。
膀胱重复畸形是罕见的疾病，几乎总是与其他先天性畸形有关。治疗取决于患者的症状和合并症，因此需要个体化治疗。
