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梅耶-罗基坦斯基-库斯特-豪泽综合征合并巨大黏液性囊腺瘤及腹股沟疝：病例报告

Mayer-Rokitansky-Kuster-Hauser syndrome complicated with giant mucinous cystadenoma and inguinal herniation: case report.

作者信息

Susilo Artha Falentin Putri, Suryawan Alfonsus Zeus, Tjandraprawira Kevin Dominique, Rachmawati Anita

机构信息

Department of Obstetrics and Gynecology, Universitas Padjadjaran, Bandung, West Java, Indonesia.

出版信息

Oxf Med Case Reports. 2024 Apr 25;2024(4):omae036. doi: 10.1093/omcr/omae036. eCollection 2024 Apr.

DOI:10.1093/omcr/omae036
PMID:38680771
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11049569/
Abstract

INTRODUCTION

Coexistence of Mayer-Rokitansky-Kuster-Hauster syndrome (MRKH) with other conditions is rare, especially when MRKH was found in a young woman presenting with ovarian malignancy. This case report wishes to highlight MRKH complicated with giant mucinous cystadenoma and bilateral inguinal hernia.

CASE REPORT

A 22-year-old nulligravid woman was admitted with primary amenorrhea and abdominal mass. Abdominal examination revealed a cystic mass 25 × 25 × 20 cm in size and a vagina 1 cm in length. Pelvic magnetic resonance imaging (MRI) showed a giant multiloculated left ovarian mass amidst the absence of uterus. During the surgery, the giant multiloculated cystic mass was identified as mucinous cystadenoma on frozen section. Bilateral medial inguinal hernia was also identified.

DISCUSSION

MRKH coexisting with other disease is rare but considering other structures arising from paramesonephric duct (PMD) may exist, allows the possibility of other structural anomalies.

CONCLUSIONS

The present report illustrates a rare case of MRKH syndrome with giant ovarian cystadenoma and inguinal hernia.

摘要

引言

迈耶-罗基坦斯基-库斯特-豪泽综合征（MRKH）与其他病症并存的情况罕见，尤其是在一名患有卵巢恶性肿瘤的年轻女性中发现MRKH时。本病例报告旨在强调MRKH合并巨大黏液性囊腺瘤和双侧腹股沟疝。

病例报告

一名22岁未孕女性因原发性闭经和腹部肿块入院。腹部检查发现一个大小为25×25×20厘米的囊性肿块，阴道长度为1厘米。盆腔磁共振成像（MRI）显示左侧有一个巨大的多房性卵巢肿块，同时未见子宫。手术中，冰冻切片显示巨大的多房性囊性肿块为黏液性囊腺瘤。还发现了双侧腹股沟内侧疝。

讨论

MRKH与其他疾病并存罕见，但考虑到可能存在由副中肾管（PMD）发育而来的其他结构，提示存在其他结构异常的可能性。

结论

本报告展示了一例罕见的MRKH综合征合并巨大卵巢囊腺瘤和腹股沟疝的病例。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a6a4/11049569/ec0c6ed188eb/omae036f4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a6a4/11049569/3ca215aa9525/omae036f1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a6a4/11049569/2b1da9c06391/omae036f2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a6a4/11049569/e8a1c50b346b/omae036f3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a6a4/11049569/ec0c6ed188eb/omae036f4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a6a4/11049569/3ca215aa9525/omae036f1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a6a4/11049569/2b1da9c06391/omae036f2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a6a4/11049569/e8a1c50b346b/omae036f3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a6a4/11049569/ec0c6ed188eb/omae036f4.jpg

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