Adrenal myelolipoma in a woman with congenital 17-hydroxylase deficiency.

A case of adrenal myelolipoma, which to our knowledge is the first case to be associated with 17-hydroxylase deficiency, is reported. This rare, benign lesion is known to occur in association with other endocrinopathies. Discussion focuses on the possible role of continued stimulation by corticotropin and/or steroids as pathogenic factors. The present case adds evidence supporting this view.